Differential Diagnosis of Otosclerosis

Differential Diagnosis: Case Scenario 1

Differential diagnosis enables a systematic, scientific approach towards patient management, enabling the audiologist to:

    - Quickly eliminate conditions, which may be life threatening
    - Gain insight in to prognosis and plan effective management
    - Provide information useful to future differential diagnoses
    - Enable the patient to understand their condition and develop coping strategies

Audiological testing

Otoscopy:

In this patient otoscopy is reported as normal, indicating that the pinna and ear canal are clear and normal and the tympanic membrane (TM) is of normal colour- translucent pearly grey, normal malleus orientation, no perforation/surgical legacy, bright cone of light, no retraction pockets or evidence of fluid accumulation.

Tuning Fork Tests:

A positive Rinne result requires AC to be reported as louder than BC. A negative Rinne result requires BC to be reported as louder than AC, indicative of conductive hearing loss (CHL). Where AC and BC are equally depreciated (e.g. in sensorineural (SNHL)/mixed (MHL) hearing loss) a false positive result is possible.

The Weber test enables the audiologist to see whether one ear is hearing better than the other. A person with CHL or SNHL would report localisation in the affected or unaffected ear respectively. A patient with a symmetric hearing loss may report central localisation and therefore an equivocal result.
In this patient a negative Rinne is reported bilaterally suggesting bilateral CHL. The Weber provided “equivocal” results, thus providing initial support for a bilateral pathology.

Pure Tone Audiometry (PTA)

In PTA the AC threshold provides information on the sensitivity of overall hearing function. The BC threshold provides a measure of integrity of cochlea function only (reflecting SNHL). Any air bone gap (ABG) provides a measure of the magnitude of CHL.

PTA for this patient shows a “mild” CHL resulting from...